ISSN: 2149-2247 | E-ISSN: 2149-2549

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Sugammadex and Genaral Anesthesia in Two Pediatric Patients with Joubert Syndrome: Case Report [Erciyes Med J]
Erciyes Med J. 2017; 39(1): 35-36 | DOI: 10.5152/etd.2017.16108

Sugammadex and Genaral Anesthesia in Two Pediatric Patients with Joubert Syndrome: Case Report

Dilek Günay Canpolat1, Mustafa Denizhan Yıldırım2, Salih Doğan3, Fatma Doğruel1, Hüseyin Per3, Mehmet Canpolat4
1Department of Oral Maxillofacial Surgery, Erciyes University Faculty of Dentistry, Kayseri, Turkey
2Department of Anesthesiology, Private Doğan Hospital, İstanbul, Turkey
3Department of Pediatric Dentistry, Erciyes University Faculty of Dentistry, Kayseri, Turkey
4Division of Pediatric Neurology, Department of Pediatrics, Erciyes University Faculty of Medicine, Kayseri, Turkey

Joubert syndrome (JS) is a rare genetic disorder that affects the cerebellum, controlling balance, and coordination, and it usually presents a molar tooth sign on magnetic resonance imaging. It is characterized by ataxia, an abnormal breathing pattern referred to as hyperpnea, sleep apnea, hypotonia, and abnormal eye and tongue movements. Because of sensitivity to respiratory depressant agents, including opiates, nitrous oxide, and neuromuscular blockers, and potential difficult airways, anesthetic management requires attention. Sugammadex binds to rocuronium and is a reverse neuromuscular blocker. In this study, two cases of JS where sugammadex was used for general anesthesia are presented. Sugammadex may be a safe general anesthetic for patients with JS.

Keywords: General anesthesia, sugammadex, Joubert syndrome

Dilek Günay Canpolat, Mustafa Denizhan Yıldırım, Salih Doğan, Fatma Doğruel, Hüseyin Per, Mehmet Canpolat. Sugammadex and Genaral Anesthesia in Two Pediatric Patients with Joubert Syndrome: Case Report. Erciyes Med J. 2017; 39(1): 35-36

Corresponding Author: Dilek Günay Canpolat, Türkiye
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